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Case
Summary
Diagnosis: Fibrous Dysplasia
Clinical hints:
This developmental bone dysplasia may be mono-ostotic or
polyostotic. In females, polyostotic disease, with cafe au
lait spots and sexual precocity is called Albright's syndrome.
Deformities and pathologic fractures are common.
Radiological Pearls:
- cystic expansion of bones
- "ground glass" appearance
- skull deformities ("leontiasis")
- rarely cranial nerve involvement
Films were kindly provided by Dr. G. Cooke.
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